A paediatric form of dermatomyositis
PC
Clinical features include:
- Fatigue
- Joint pain
- Weakness of proximal muscles
- Malar rash
- Heliotrope rash over eyelids
Investigations
Bloods may show:
- Raised ESR
- Raised creatine kinase (CK)
In addition to bloods indicating JDM, diagnoses can be confirmed via:
- MRI scans showing muscle oedema
- Muscle biopsies
- Nailfold capillaroscopy showing microangiopathy
Management